Journal of Craniomaxillofacial Research 2017. 4(2):377-382.

Ectodermal dysplasia: A report of two cases
Mozhgan Kazemian, Farnoosh Razmara, Nafiseh Ghadiri Moghadam

Abstract


Introduction: Ectodermal dysplasia (ED) is a group of syndromes and disorders in the human body characterized by structural anomalies in the ectoderm and often associated with hair, teeth
and skin abnormalities. There are many syndromes associated with ED.
Case report: Here is a case report of two young patients with different manifestations of ectodermal dysplasia.
Conclusion: One patient was diagnosed as Rapp-Hodgkin syndrome and the other as Hypohidrotic ectodermal dysplasia, according to clinical findings.
Key words: Ectodermal dysplasia, Hypodontia, Hypohydrotia.

Keywords


Ectodermal dysplasia; Hypodontia; Hypohydrotia.

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References


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